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OTHER PROBLEMS IN BIG FASCIAL
HAEMANGIOMAS
In some instances haemangiomas might have been a part of a disease of the
whole body. Sometimes the type, location and number of the haemangiomas
make us to think about these diseases. The most important one of these dia-
seases is called PHACE (s) syndrome in medicine. In this disease, besides the
haemangioma in the face, there are abnormal vascular lesions in the back part
of the brain, at the vessels going out of the heart and the vessels of the eye.
In this condition, propranolol only is effective in fascial haemangioma and
does not have effect in other lesions. It is important that the drug should be
given very carefully in this disease because of the abnormalities in the brain
vessels. If treatment is mandatory, early MR-angiography has no or limited
benefit. In every condition the treatment should be applied carefully.
He has hyperemia in his left part of face at birth. It became prominent by time. It was swollen from
the skin surface at the last 3 to 4 months before admission. There was bleeding from the back of his
ear. The doctors said that they could do nothing until he was 6 years-old. He was the most severe
case of all we had seen. We thought that there might be other components. Propranolol was started in a
small dose. He was hospitalized longer than other patients, the dose of the drug was increased gradual-
ly. The treatment response was great in this patient. After treatment a special MR (MRI-angiography) I
for the vessels of brain was performed. There were abnormal vessels on the left side of the brain.
Case Story
E. Y.
Birth Date : 13.03.2012
Admission Date: 12.05.2012
Age at Diagnosis: 2 months
City
: Iğdır
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